11. Clinical features may vary but commonly include Cholangitis , hepatomegaly and signs of portal hypertension. 12. In this clogged state, the duct is especially vulnerable to an infection called ascending cholangitis . 13. The most common bacteria linked to ascending cholangitis are cocci, Enterococcus causes 10 20 %. 14. Fever indicates a complicating bacterial cholangitis . 15. With primary sclerosing cholangitis , believed genetic in origin, your immune system attacks your bile ducts. 16. Morbidity is common and is caused by complications of cholangitis , sepsis, choledocholithiasis, and cholangiocarcinoma. 17. Type 1 is associated with pancreatitis, Sjogren syndrome, Primary sclerosing cholangitis and Inflammatory bowel disease. 18. Rarely are diseases of the bile ducts, such as primary sclerosing cholangitis , causes of cirrhosis. 19. The free or " unchaperoned " bile acids in bile of patients with MDR3 deficiency cause a cholangitis . 20. "' Ductopenia "'refers to a reduction in the number of primary biliary cholangitis .
